A case of anomalous aortic origin of coronary artery associated with a coved-type electrocardiogram

J Cardiovasc Electrophysiol. 2021 Feb;32(2):554-557. doi: 10.1111/jce.14872. Epub 2021 Jan 19.

Abstract

Brugada syndrome (BrS) is a sudden cardiac death syndrome characterized by a coved-type electrocardiogram (ECG). Different disorders, such as ischemia, can emulate a Brugada-pattern ECG (Brugada phenocopy). We report herein, the first case of surgical epicardial electrophysiological mapping in a successfully resuscitated patient with an anomalous aortic origin of the coronary artery (AAOCA) associated with a coved-type ECG. It was debatable whether the coved-type ECG and the abnormal arrhythmogenic substrate in the epicardial right ventricular outflow tract were derived from BrS or from repetitive ischemia due to AAOCA; however, the epicardial electrophysiological mapping helped in deciding the treatment strategy.

Keywords: Brugada phenocopy; Brugada syndrome; ablation; anomalous aortic origin of a coronary artery; ventricular fibrillation.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Brugada Syndrome* / complications
  • Brugada Syndrome* / diagnosis
  • Coronary Vessels*
  • Death, Sudden, Cardiac / etiology
  • Electrocardiography
  • Epicardial Mapping
  • Humans