Ventricular Septal Myectomy for the Treatment of Left Ventricular Outflow Tract Obstruction Due to Fabry Disease

Bharath Raju; Charles S Roberts; Mohanakrishnan Sathyamoorthy; Raphael Schiffman; Caren Swift; Peter A McCullough

doi:10.1016/j.amjcard.2020.07.020

Ventricular Septal Myectomy for the Treatment of Left Ventricular Outflow Tract Obstruction Due to Fabry Disease

Am J Cardiol. 2020 Oct 1:132:160-164. doi: 10.1016/j.amjcard.2020.07.020. Epub 2020 Jul 13.

Authors

Bharath Raju¹, Charles S Roberts¹, Mohanakrishnan Sathyamoorthy², Raphael Schiffman³, Caren Swift⁴, Peter A McCullough⁵

Affiliations

¹ Baylor University Medical Center, Dallas, Texas; Baylor Jack and Jane Hamilton Heart and Vascular Hospital, Dallas, Texas; Baylor Heart and Vascular Institute, Dallas, Texas.
² Baylor Scott and White All Saints Medical Center, Fort Worth Texas; University of North Texas-Texas Christian University School of Medicine, Fort Worth Texas.
³ Baylor Kimberly H. Courtwright and Joseph W. Summers Institute of Metabolic Disease, Fort Worth Texas.
⁴ Baylor University Medical Center, Dallas, Texas.
⁵ Baylor University Medical Center, Dallas, Texas; Baylor Jack and Jane Hamilton Heart and Vascular Hospital, Dallas, Texas; Baylor Heart and Vascular Institute, Dallas, Texas. Electronic address: peteramccullough@gmail.com.

PMID: 32773220
DOI: 10.1016/j.amjcard.2020.07.020

Abstract

Fabry cardiomyopathy can cause symptomatic left ventricular outflow tract obstruction. We review a case of Fabry cardiomyopathy mimicking hypertrophic cardiomyopathy on echocardiography with severe left ventricular outflow tract obstruction treated with ventricular septal myectomy.

Publication types

Case Reports

MeSH terms

Adult
Cardiac Surgical Procedures / methods*
Echocardiography
Fabry Disease / complications*
Fabry Disease / diagnosis
Humans
Magnetic Resonance Imaging, Cine / methods
Male
Ventricular Outflow Obstruction / diagnosis
Ventricular Outflow Obstruction / etiology
Ventricular Outflow Obstruction / surgery*
Ventricular Septum / diagnostic imaging
Ventricular Septum / surgery*