Hybrid trans-apical atrioventricular valve-in-valve implantation in Fontan circulation

Catheter Cardiovasc Interv. 2020 Apr 1;95(5):950-953. doi: 10.1002/ccd.28714. Epub 2020 Jan 8.

Abstract

Trans-apical approach has been proved successful in failing surgical bio-prosthesis in both mitral and aortic position in adult patients. Recently, valve-in-valve treatments have been applied even in patients with complex congenital heart disease. Here, we report the case of a 32 years old lady with left atrial isomerism, complete AV septal defect, interrupted inferior vena cava with azygos continuation who underwent Kawashima procedure with atrial Fontan. Severe systemic atrioventricular valve regurgitation necessitated a 33 mm Perimount valve implantation and conversion to lateral tunnel Fontan. After only 4 years there was severe valve stenosis and the patient underwent successful trans-apical transcatheter implantation of a 29 mm Sapien valve.

Keywords: Fontan circulation; atrioventricular valve replacement; total cavopulmonary connection; transcatheter valve-in-valve implantation.

Publication types

  • Case Reports
  • Video-Audio Media

MeSH terms

  • Adult
  • Cardiac Catheterization / instrumentation*
  • Female
  • Fontan Procedure* / adverse effects
  • Heart Defects, Congenital / diagnostic imaging
  • Heart Defects, Congenital / physiopathology
  • Heart Defects, Congenital / surgery*
  • Heart Valve Prosthesis Implantation / adverse effects
  • Heart Valve Prosthesis Implantation / instrumentation*
  • Heart Valve Prosthesis*
  • Humans
  • Prosthesis Design
  • Recovery of Function
  • Treatment Outcome
  • Tricuspid Valve / diagnostic imaging
  • Tricuspid Valve / physiopathology
  • Tricuspid Valve / surgery*
  • Tricuspid Valve Insufficiency / diagnostic imaging
  • Tricuspid Valve Insufficiency / etiology
  • Tricuspid Valve Insufficiency / physiopathology
  • Tricuspid Valve Insufficiency / surgery*
  • Tricuspid Valve Stenosis / diagnostic imaging
  • Tricuspid Valve Stenosis / etiology
  • Tricuspid Valve Stenosis / physiopathology
  • Tricuspid Valve Stenosis / surgery*