The Journal of Thoracic and Cardiovascular Surgery
Volume 160, Issue 5, November 2020, Pages 1166-1175
Adult: AortaManagement of the aortic arch in patients with Loeys–Dietz syndrome
Under an Elsevier user license
open archive
Graphical abstract
Findings of the study: The need for subsequent arch interventions after acute aortic dissection (AAD) does not seem to be greater in patients with Loeys–Dietz syndrome (LDS) compared with Marfan syndrome (MFS). In contrast, patients with LDS undergoing elective root repair have an increased risk for subsequent arch interventions, so consideration should be given to complete removal of the distal ascending aorta.
Key Words
aortic surgery
Marfan syndrome
Loeys–Dietz syndrome
aortic arch
acute aortic dissection
connective tissue disorders
Abbreviations and Acronyms
AAD
acute aortic dissection
CI
confidence interval
HAR
hemiarch replacement
JHH
Johns Hopkins Hospital
LDS
Loeys–Dietz syndrome
MFS
Marfan syndrome
SHR
subhazard ratio
TAR
total aortic arch replacement
Cited by (0)
Read at the 2016 American Association for Thoracic Surgery Aortic Symposium, New York, New York, and recipient of the Randall Griepp Award.
© 2019 Published by Elsevier Inc. on behalf of The American Association for Thoracic Surgery